label: Orbital IgG4-Related Disease
label_lc: orbital igg4-related disease
description: A mass-forming lesion that affects the orbit and is characterized by the presence of a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells and storiform tissue fibrosis, and increased serum IgG4 levels. It responds to steroids treatment and follows a course of remissions and recurrences.