label: Inborn Error of Immunity-Associated Cutaneous T-Cell Lymphoproliferative Disorder
label_lc: inborn error of immunity-associated cutaneous t-cell lymphoproliferative disorder
description: A cutaneous EBV-negative lymphoproliferative disorder that is composed of CD8-positive T-cells and is associated with inborn immunodeficiency. The cutaneous manifestations include generalized papulo-nodular indurated lesions. It infrequently affects the subcutaneous tissue, lungs, bone marrow, and gastrointestinal tract as well. It has a variable clinical course.