label: Central Nervous System Neuroblastoma, FOXR2-Activated
label_lc: central nervous system neuroblastoma, foxr2-activated
description: A rare central nervous system neoplasm with neuroblastic and/or neuronal differentiation that arises from the supratentorial brain. It is characterized by the presence of structural rearrangements of FOXR2 gene that result in the activation of the transcription factor FOXR2.