label: Hermansky-Pudlak syndrome with pulmonary fibrosis
label_lc: hermansky-pudlak syndrome with pulmonary fibrosis
description: Hermansky-Pudlak syndrome with pulmonary fibrosis as a complication includes two types (HPS-1 and HPS-4) of Hermansky-Pudlak syndrome (HPS), a multi-system disorder characterized by oculocutaneous albinism, bleeding diathesis and, in some cases, pulmonary fibrosis or granulomatous colitis.