label: Pineoblastoma miRNA Processing Altered 2
label_lc: pineoblastoma mirna processing altered 2
description: Pineoblastoma characterized by alterations in genes involved in miRNA biogenesis (DICER1, DROSHA, and DGCR8). It may manifest as a sporadic tumor or part of DICER1 syndrome. It affects older children and follows a more favorable course.