label: Desmoplastic Small Round Cell Tumor
label_lc: desmoplastic small round cell tumor
description: An aggressive malignant soft tissue neoplasm of uncertain differentiation.  It is characterized by a recurrent chromosomal translocation t(11;22)(p13;q12) and the presence of small round cells in a desmoplastic stroma.  It usually affects children and young adults.  The most common site of involvement is the abdomen.  Patients usually present with abdominal distention, pain, ascites, and a palpable abdominal mass.  The prognosis is usually poor.