label: SMARCB1-Deficient Sinonasal Adenocarcinoma
label_lc: smarcb1-deficient sinonasal adenocarcinoma
description: An SWI/SNF-deficient sinonasal carcinoma characterized by inactivating mutation of SMARCB1 gene. It usually affects the nasal sinuses. It is composed of malignant epithelial cells with a predominantly oncocytoid/plasmacytoid morphology and prominent glandular formations.