label: SMARCB1-Deficient Sinonasal Carcinoma
label_lc: smarcb1-deficient sinonasal carcinoma
description: "An SWI/SNF-deficient sinonasal carcinoma characterized by biallelic deletion or inactivating mutation of SMARCB1 gene. It usually affects the paranasal sinuses, especially ethmoid. It is composed of a monomorphic malignant epithelial cellular population with a predominantly basaloid or plasmacytoid/rhabdoid morphology."