label: Epithelioid Sarcoma
label_lc: epithelioid sarcoma
description: "An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns.  The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern.  It usually occurs in young adults.  The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma)."