label: Composite Gangliocytoma/Neuroma and Neuroendocrine Tumor
label_lc: composite gangliocytoma/neuroma and neuroendocrine tumor
description: "A usually indolent neuroendocrine neoplasm that almost exclusively arises in the second part of the duodenum. Rare sites of involvement include jejunum, pylorus, appendix, thymus, and lung. It is a triphasic tumor consisting of a mixture of epithelioid neuroendocrine cells, Schwann-like cells, and ganglion cell-like elements."