label: glycogen storage disorder due to hepatic glycogen synthase deficiency
label_lc: glycogen storage disorder due to hepatic glycogen synthase deficiency
description: "Glycogen synthetase deficiency, or glycogen storage disease (GSD) type 0, is a genetically inherited anomaly of glycogen metabolism and a form of GSD characterized by fasting hypoglycemia. This is not a glycogenosis, strictly speaking, as the enzyme deficiency decreases glycogen reserves."