label: diaphyseal medullary stenosis-bone malignancy syndrome
label_lc: diaphyseal medullary stenosis-bone malignancy syndrome
description: "Diaphyseal medullary stenosis with malignant fibrous histiocytoma is a very rare autosomal dominant bone dysplasia/cancer syndrome characterized clinically by bone infarctions, cortical growth abnormalities, pathological fractures, and development of bone sarcoma (malignant fibrous histiocytoma)."