label: Ductus venosus agenesis with extrahepatic drainage and liver bypass
label_lc: ductus venosus agenesis with extrahepatic drainage and liver bypass
description: "A form of ductus venosus agenesis in which umbilical vein does not connect to the portal venous system. The liver is bypassed and the umbilical vein drains into a systemic vein such as the inferior vena cava. This variant has been reported to have an unfavorable prognosis due to a presumed association with congestive heart failure and hydrops."