label: Reduced peroxisomal glutaryl-CoA oxidase activity
label_lc: reduced peroxisomal glutaryl-coa oxidase activity
description: "Diminished enzyme activity of peroxisomal glutaryl-CoA oxidase, an enzyme that metabolizes glutaryl-CoA (a metabolite of L-lysine, L-hydroxy-lysine and L-tryptophan) by dehydrogenation to glutaconyl-CoA directly followed by decarboxylation of this to crotonyl-CoA."